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| CLINICAL QUIZ |
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| Year : 2019 | Volume
: 12
| Issue : 2 | Page : 141 |
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The golden ring
Simar Rajan Singh, Sonam Yangzes, Jagat Ram
Department of Ophthalmology, Advanced Eye Centre, Post Graduate Institute of Medical Education and Research, Chandigarh, India
| Date of Web Publication | 4-Jun-2019 |
Correspondence Address:
Dr. Jagat Ram
Department of Ophthalmology, Advanced Eye Centre, Post Graduate Institute of Medical Education and Research, Sector 12, Chandigarh
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/ojo.OJO_172_2018
How to cite this article:
Singh SR, Yangzes S, Ram J. The golden ring. Oman J Ophthalmol 2019;12:141 |
 Case Presentation | |  |
Afemale in her mid-20s presented to the ophthalmologist with low vision in both eyes since childhood. On examination, she had a best-corrected visual acuity of 20/80 in the right eye with 17.00 Ds and 20/40 in the left eye with 14.00 Ds. Intraocular pressures were normal. On close inspection, both eyes [Figure 1] (Panel A – right eye, Panel B – left eye) had thick lenses with 360° golden ring around the lens on retroillumination. Posterior segment examination was unremarkable. Systemic examination revealed a short stature, brachydactyly, and joint stiffness. | Figure 1: Anterior segment photograph in retroillumination of the right (Panel a) and left (Panel b) eyes of a patient demonstrating a round spherical lens with a golden ring
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| Questions | | |
- What is the ocular diagnosis?
- Subluxated lens
- Microspherophakia
- Keratoconus
- Lenticonus
- Which of the following syndromes are most commonly associated with this abnormality?
- Marfan's syndrome
- Alport syndrome
- Weill–Marchesani syndrome
- Ehlers–Danlos syndrome
- What is the best surgical management for this patient?
- Clear lens extraction with intraocular lens implantation
- Laser-assisted in situ keratomileusis
- Penetrating keratoplasty
- Implantable Collamer Lens
 View Answer
[TAG:2]Answers[/TAG:2] - b
- c
- a
[TAG:2]Case Description[/TAG:2] This is a case of microspherophakia with Weill–Marchesani Syndrome. Microspherophakia is a lenticular abnormality in which the existing zonules lack tension that directly contributes to the presence of a small spherical lens. [1] The laxity of the zonules may lead to anterior subluxation of the lens which can cause uneven shallowing of the anterior chamber, sometimes even leading to raised intraocular pressure. [2],[3] In a dilated pupil, the margin of the crystalline lens can be seen as a golden ring on retroillumination. This condition must be ruled out in all cases of high myopic refractive error with a dilated slit lamp examination. Surgical intervention may be required in cases of high refractive error, lens subluxation or glaucoma. This patient was managed with sequential clear lens extraction with in-the-bag intraocular lens implantation and capsular tension segments. [4] She maintains an unaided vision of 20/30 in both eyes after 1-year follow-up. Declaration of patient consentThe authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed. Financial support and sponsorshipNil. Conflicts of interestThere are no conflicts of interest.
[Figure 1]
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